A vascular ring is a congenital defect in which there is an abnormal formation of the aorta and/or its surrounding blood vessels. The trachea and esophagus are completely encircled and sometimes compressed by a "ring" formed by these vessels, which can lead to breathing and digestive difficulties. Most often this is because of persistence of the double aortic arch after the second month of fetal life. The two arches surround the esophagus and trachea which if sufficiently constrictive cause the breathing or swallowing difficulties. A less common ring is present with a right aortic arch instead of the usual left-sided aortic arch which compresses the esophagus and trachea because of the persistence of a ductal ligament (from fetal circulation) that may connect between the aorta on the front and the left subclavian artery posteriorly going to the left arm.
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Congenital malformations and deformations of circulatory system (Q20-Q28, 745-747) |
| Cardiac chambers and connections |
Persistent truncus arteriosus - Double outlet right ventricle (Taussig-Bing syndrome) - Transposition of the great vessels (dextro, levo) |
| Cardiac septa |
Ventricular septal defect - Atrial septal defect (Lutembacher's syndrome) - Atrioventricular septal defect (Ostium primum) - Tetralogy of Fallot - Eisenmenger's syndrome |
| Right: pulmonary and tricuspid valves |
pulmonary valves (stenosis, insufficiency) - tricuspid valves (stenosis, atresia) - Ebstein's anomaly |
| Left: aortic and mitral valves |
aortic valves (stenosis, insufficiency, bicuspid) - mitral valves (stenosis, regurgitation) - Hypoplastic left heart syndrome |
Other congenital malformations
of heart |
Dextrocardia - Levocardia - Cor triatriatum |
| Great arteries |
aorta (Patent ductus arteriosus, Aortic coarctation, Interrupted aortic arch, Overriding aorta, Aneurysm of sinus of Valsalva, Vascular ring) - Pulmonary atresia |
| Great veins |
Persistent left superior vena cava - Total anomalous pulmonary venous connection - Scimitar syndrome |
| Other |
Arteriovenous malformation (Cerebral arteriovenous malformation) |
| See also non-congenital conditions (I, 390-459) |
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